Erdheim-Chester disease. Report of one case

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dc.contributor.authorVega, Jorge
dc.contributor.authorCisternas, Marcela
dc.contributor.authorBergoeing, Michel
dc.contributor.authorEspinosa, Roberto
dc.contributor.authorZapico, Alvaro
dc.contributor.authorChadid, Pedro
dc.contributor.authorSantamarina, Mario
dc.date.accessioned2024-01-10T12:38:45Z
dc.date.available2024-01-10T12:38:45Z
dc.date.issued2011
dc.description.abstractWe report a 76-year-old male who was admitted due to progressive congestive heart failure lasting several months. An echocardiogram showed a large pericardial effusion with early signs of pericardial tamponade and an irregular surface suggestive of cancer infiltration. The patient was operated, creating a pericardial window and draining 1,200 ml of a brownish yellow fluid with abundant cellularity. Pericardial biopsy showed infiltration by CD68 (+), CD1a (-) and S100 (-) cells. Twenty-eight months earlier, due to fatigue, dyspnea, and a non-specific inflammatory process, an enhanced-contrast-scan showed that aorta was coated with a hypodense tissue that began near the aortic valve and extended until the inferior mesenteric artery, with stenosis of the left subclavian, celiac axis, renal and upper mesenteric arteries. An angioplasty and stent placing was carried out in the last two arteries. Both kidneys had the appearance of "hairy kidneys". A bone scan showed increased uptake in femurs and tibiae and X-ray examination showed osteosclerosis in metaphysis and diaphysis. The diagnosis of Erdheim-Chester disease (non-Langerhans-cell histiocytosis) was made and the patient was treated with steroids and methotrexate. (Rev Med Chile 2011; 139: 1054-1059).
dc.format.extent6 páginas
dc.fuente.origenWOS
dc.identifier.issn0034-9887
dc.identifier.pubmedidMEDLINE:22215336
dc.identifier.urihttps://repositorio.uc.cl/handle/11534/77094
dc.identifier.wosidWOS:000295186900011
dc.information.autorucMedicina;Bergoeing M ;S/I;92603
dc.information.autorucMedicina;Cisternas M ;S/I;4233
dc.issue.numero8
dc.language.isoes
dc.nota.accesoSin adjunto
dc.pagina.final1059
dc.pagina.inicio1054
dc.publisherSOC MEDICA SANTIAGO
dc.revistaREVISTA MEDICA DE CHILE
dc.rightsregistro bibliográfico
dc.subjectErdheim-Chester disease
dc.subjectCardiac tamponade
dc.subjectHistiocytosis
dc.subjectnon-Langerhans
dc.subjectPericardial effusion
dc.subjectCARDIAC INVOLVEMENT
dc.subjectMAGNETIC-RESONANCE
dc.subject.ods03 Good Health and Well-being
dc.subject.odspa03 Salud y bienestar
dc.titleErdheim-Chester disease. Report of one case
dc.typeartículo
dc.volumen139
sipa.codpersvinculados92603
sipa.codpersvinculados4233
sipa.indexWOS
sipa.indexScopus
sipa.trazabilidadCarga SIPA;09-01-2024
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